NGO

Repositioning drugs for a rare disease

SDSC Team:
Share this post

Context

The Sanfilippo syndrome, also known as mucopolysaccharidosis III (MPS III), is a rare genetic disease which affects 1 in every 70,000 children. Because of its neurodegenerative nature and multi-system impact, the Sanfilippo Syndrome is often called “childhood Alzheimer’s” or “childhood dementia.”

Photo of Liam, courtesy of the Fondation Sanfilippo Suisse.

This disease is classified as a lysosomal storage disorder and is divided into four subtypes (MPS III A, B, C and D). A genetic variation of the sequence coding for an enzyme results in an inability to properly break down heparan sulfate leading to its accumulation in cells and tissues. Consequently, the affected children face severe cognitive decline, seizures, movement and multiple organs disorders and ultimately death around their early teens.

Albeit important research efforts, no treatment is approved to date. Interventions intended to repair mutated gene(s) causing the syndrome, or to replace defective enzymes are being explored. Researchers also investigate drugs capable of restoring the normal functioning of patient's nervous cells to attenuate or remove the disease's symptoms. Finding these drugs is however a tenuous and lengthy process.

Objectives

The Swiss Data Science Center is collaborating with theFondation Sanfilippo Suisse based in Geneva to further accelerate the discovery and approval of treatment against this disease. The main objectives of this collaboration are:

  • Build a deep learning framework to characterize and predict associations between human diseases and the drugs approved to treat them.
  • Generate a list of candidate drugs to repurpose for the treatment of the Sanfilippo syndrome, from a large pool drugs initially indicated against other diseases.
  • Refine this list by incorporating feedback from experts, before further validation by lab testing.  

Benefits

A systematic screening of approved drugs susceptible to affect the Sanfilippo disease's causes or symptoms will greatly accelerate the development of a treatment. Repurposed drugs are subject to faster clinical research cycles relative to newly developed drugs, decreasing both the time and money needed to make them accessible to affected children.

Notes

We thank Fondation Sanfilippo Suisse for the provided funding and the scientific  expertise and guidance provided by Nicolas Lantz of the Fondation’s Scientific Committee that moves forward this project to obtain first results and drug candidates for further testing in MPS III context by mid 2024.

Links

More case studies

Public Sector

Enhancing Parliamentary Services with Generative AI

Partly motivated by Inter-Parliamentary Union directives, the Swiss Parliament departments are exploring uses of generative AI in collaboration with academic institutions. The SDSC team was mandated to create a custom chat assistant powered by state-of-the-art LLMs and a robust RAG system to support complex multilingual interactions for information retrieval.
Private sector

An artificial intelligence-based system for augmented cell & gene therapies

Tigen is a clinical-stage biotech company, founded in 2017 and based in Switzerland, with a mission to bridge the gap between academic research and commercially viable therapies, particularly in the field of T cell-based cancer treatments.
Private sector

Qlaire: Enhance Quality Management with generative AI

Qlaire enables Bühler's quality experts to rapidly access knowledge from issues texts. This leads to faster resolution of issues, easier retrieval of existing solutions, more efficient identification of quality hotspots, and a deeper understanding of quality concerns.

Contact us

Let’s talk Data Science

Do you need our services or expertise?
Contact us for your next Data Science project!